Transfusions to maintain a hematocrit of more than 36 percent do not reduce complications of pregnancy.In surgical settings, simple transfusions to increase hemoglobin (Hb) levels to 10 g/dL are as good as or safer than aggressive transfusions to reduce sickle hemoglobin (Hb S) levels to below 30 percent.Pneumococcal vaccine prevents pneumococcal infection in children.Penicillin prophylaxis prevents pneumococcal sepsis in children.The practice guidelines best supported by scientific evidence are: pdf icon The Management of Sickle Cell Diseaseįrom the National Heart Lung and Blood Institute (NHLBI), 2014 Treat pain of patients with SCD promptly. It is essential that every child with SCD receive comprehensive care that is coordinated through a medical home with appropriate expertise.
Timely and appropriate treatment of acute illness is critical, because life-threatening complications develop rapidly. The provision of comprehensive care is a time-intensive endeavor that includes ongoing patient and family education, periodic comprehensive evaluations and other disease-specific health maintenance services, psychosocial care, and genetic counseling. Specialized comprehensive medical care decreases morbidity and mortality during childhood. This statement provides pediatricians in primary care and subspecialty practice with an overview of the genetics, diagnosis, clinical manifestations, and treatment of SCD. Health Supervision for Children with Sickle Cell Diseaseįrom the American Academy of Pediatrics (AAP), 2011 Stem Cell Transplantation external icon.
The recommendations address treatment of both adult and pediatric SCD. ASH formed a committee of medical experts, researchers and patients to review evidence and form recommendations on SCD. In 2016, the American Society of Hematology (ASH) initiated an effort to develop clinical practice guidelines on Sickle Cell Disease (SCD). ASH Clinical Practice Guidelines on Sickle Cell Disease
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